
PROGRAM MENU
EDUCATIONAL PROGRAM
PRE-SUMMIT WORKSHOPS
SATELLITE SYMPOSIA
Educational Program
THSNA programming is focused on presenting the most current issues in Hemostasis and Thrombosis. THSNA 2022 will include daily plenary sessions (without other concurrent sessions); four educational tracks, a Pre-Summit Workshop Day, daily ePoster sessions, oral abstract presentations of original research and an exhibit hall with commercial booths.
TUESDAY, AUGUST 16
7:15 - 8:15 AM
SATELLITE SYMPOSIUM
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ARE HIGHER FACTOR LEVELS A RISING CONSIDERATION WHEN SELECTING A HEMOPHILIA TREATMENT? (SPONSORED BY NOVO NORDISK, INC. ) Chicago Ballroom VI This program will discuss the clinical relevance of reaching high factor activity levels in patients with hemophilia. An increased risk of bleeding episodes exists with time spent at low factor activity levels, and the World Federation of Hemophilia recognizes the importance of high factor activity levels and maintaining hemostasis in patients with hemophilia. The pharmacokinetic and clinical characteristics of products used to treat patients with hemophilia will also be presented. Click Here to take the post survey. |
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NEW CLINICAL DATA FOR PROPHYLAXIS IN VON WILLEBRAND DISEASE AND HEMOPHILIA A (SPONSORED BY OCTAPHARMA AG) Chicago Ballroom IX-X Join Jill Johnsen, Robert Sidonio and Craig Kessler for this symposium putting prophylaxis under the spotlight and presenting new clinical data and ongoing investigations for its use in people with von Willebrand disease (VWD) and hemophilia A. The potential for prophylaxis to offer optimal bleed protection in people with VWD will be discussed, supported by new clinical data from a recently completed prospective trial of prophylaxis with a von Willebrand factor/coagulation factor VIII (VWF/FVIII) concentrate. Next generation sequencing (NGS) is a powerful tool whose use to characterize VWF mutations may improve VWD diagnosis and management. In people with severe hemophilia A, prophylaxis is widely accepted as the standard of care, and should be personalized to the patients needs. However, the lack of head-to-head studies of different FVIII products makes it challenging to make informed treatment decisions. Insights into the relative effects of different products can be obtained through indirect comparisons using validated statistical methodology. The results of such a comparison of personalized prophylaxis studies in hemophilia A will be presented and discussed. The differential binding capacity for rFVIII concentrates could have implications in platelet biology and new scientific data will be presented. |
8:30 - 9:45 AM
PLENARY SESSION
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PATIENT CENTERED OUTCOMES Chair/Organizer: Cathy Hayward, Vinai Bhagirath Sheraton Ballroom IV-V |
INTRODUCTION VIDEO. |
8:30 |
PATIENT CENTERED OUTCOMES RESEARCH - PCORI METHODOLOGY Mark Skinner. Institute for Policy Advancement Ltd. |
8:50 |
PATIENT CENTERED RESEARCH - THROMBOSIS Elliott Haut. Johns Hopkins Medicine |
9:10 |
PATIENT CENTERED RESEARCH - HEMOSTASIS Diane Nugent. CHOC Children's Hospital |
9:30 |
Q&A. |
9:45 - 10:45 AM
POSTERS/EXHIBITS/BREAK
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POSTERS/EXHIBITS/BREAK (click to view)
Riverwalk AB Coffee Break sponsored by Spark Therapeutics, Inc. |
A1. ANTICOAGULATION CLINICS |
101 |
LABORATORY MIMICS: A POTENT LUPUS COFACTOR EFFECT MASQUERADING AS A COAGULATION FACTOR X INHIBITOR IN A PATIENT WITH A B-CELL NEOPLASM Angela M Verdoni, PhD, DABMGG1, Nicoletta Machin, DO2, 3, Michael Meyer, MSc1, Donald Woytowitz, MD2, 3, Margaret Ragni, MD, MPH2, 3, Franklin Bontempo, MD1, 2, 3, Jansen Seheult, MB BCh BAO, MSc, MD1, 4, Irina Chibisov, MD1, 5. 1Vitalant Specialty Labs, Pittsburgh, PA, USA. 2Department of Medicine, University of Pittsburgh Medical Center, Pittsburgh, PA, USA. 3Department of Medicine, Division of Hematology/Oncology, University of Pittsburgh, Pittsburgh, PA, USA. 4Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USA. 5Department of Pathology, University of Pittsburgh, Pittsburgh, PA, USA |
A2. PLATELET ACTIVATION AND BIOCHEMISTRY |
102 |
IMER, A NATURALLY OCCURRING MERTK SPLICE VARIANT, INHIBITS PLATELET AGGREGATION BY TRAPPING GAS6 Adam Kidwell1, 2, Stephanie Springborn1, Peter Newman1, Jorge DiPaola3, Deborah DeRyckere4, 5, Douglas K Graham4, 5, Brian R Branchford1, 2. 1Versiti Blood Research Institute, Wauwatosa, WI, USA. 2Medical College of Wisconsin, Department of Pediatrics, Wauwatosa, WI, USA. 3Washington University School of Medicine, Department of Pediatrics, St. Louis, MO, USA. 4Aflac Cancer a Blood Disorders Center, Children's Healthcare of Atlanta, Atlanta, GA, USA. 5Emory University School of Medicine, Department of Pediatrics, Atlanta, GA, USA |
A4. DISORDERS OF PLATELET NUMBER OR FUNCTION |
103 |
UNIQUE CASE OF REFRACTORY THROMBOTIC THROMBOCYTOPENIC PURPURA DUE TO UNDIAGNOSED SJOGREN'S SYNDROME Syed Kamran, Mimi Baber, Joud Zakhour. University of Kansas, Wichita, KS, USA |
104 |
THE EFFECT OF CHRONIC LYMPHOCYTIC LEUKEMIA IN HOSPITALIZED IMMUNE THROMBOCYTOPENIA PATIENTS: A NATIONWIDE ANALYSIS. Ekrem Turk1, Khaldun Obeidat1, Yasin Goksu2. 1John H. Stroger, Jr. Hospital of Cook County, Chicago, IL, USA. 2University of Illinois at Chicago, Department of Pathology, Chicago, IL, USA |
A5. BLOOD COAGULATION AND FIBRINOLYTIC FACTORS |
105 |
DEFINING THE IMPACT OF SOCIAL DRIVERS ON HEALTH OUTCOMES FOR PEOPLE WITH INHERITED BLEEDING DISORDERS Karina Lopez1, Keri Norris1, Marci Hardy1, Leonard A. Valentino1, 2. 1National Hemophilia Foundation, New York, NY, USA. 2Rush University, Chicago, IL, USA |
106 |
EVALUATION OF INHIBITORS EFFECT ON PLASMIN'S AMIDOLYTIC AND FIBRINOLYTIC ACTIVITY USING S-2251 AND ANNULAR FIBRIN CLOT ASSAYS Tanmaye Nallan Chakravarthula1, 2, Liliana Patino1, Ziqian Zeng1, 2, Nathan J. Alves1, 2. 1Department of Emergency Medicine, Indiana University School of Medicine, Indianapolis, IN, USA. 2Weldon School of Biomedical Engineering, Purdue University, West Lafayette, IN, USA |
A6. DISORDERS OF COAGULATION OR FIBRINOLYSIS |
107 |
ASSOCIATION OF HYPONATREMIA WITH CLINICAL OUTCOMES IN PATIENTS ADMITTED WITH ACUTE PULMONARY EMBOLISM: ANALYSIS OF THE NATIONAL INPATIENT SAMPLE VAISHALI DEENADAYALAN MD, DENNIS DANSO KUMI MD, BIRJU PATEL MD. John H Stroger Jr Hospital of Cook County, Chicago, IL, USA |
108 |
DEFINING THE EPITOPE SPECIFICITY OF THE EARLY IGM RESPONSE TO FACTOR VIII IN HEMOPHILIA A MICE Saeyeon Ju1, Wallace Hunter Baldwin2, Courtney Cox2, Shannon L Meeks2, Seema R Patel2. 1Emory University, Atlanta, GA, USA. 2Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta/Emory University School of Medicine, Atlanta, GA, USA |
109 |
PROPHYLAXIS WITH RECOMBINANT VON WILLEBRAND FACTOR IN PATIENTS WITH TYPE 3 VON WILLEBRAND DISEASE: POST HOC ANALYSIS FROM A PHASE 3 TRIAL Frank W. G. Leebeek1, Miguel Escobar2, Andreas Tiede3, Michael Wang4, Bulent Zulfikar5, Scarlett Wang6, Yi Wang6, Gulden Ozen6. 1Department of Hematology, Erasmus MC, University Medical Center, Rotterdam, Netherlands. 2University of Texas Health Science Center at Houston, Houston, TX, USA. 3Hannover Medical School, Department of Hematology, Hemostasis, Oncology and Stem Cell Transplantation, Hannover, Germany. 4Hemophilia and Thrombosis Center, University of Colorado Anschutz Medical Campus, Aurora, CO, USA. 5Department of Pediatric Hematology/Oncology, Istanbul University Oncology Institute, Istanbul, Turkey. 6Takeda Development Center Americas, Inc, Cambridge, MA, USA |
110 |
PATHOLOGIST-DIRECTED REFLEXIVE EVALUATION OF PROLONGED CLOTTING TIMES: A NATIONAL REFERENCE LABORATORY EXPERIENCE. Karen A Moser1, 2, Ming Y Lim3, Kristi J Smock1, 2. 1Department of Pathology, University of Utah, Salt Lake City, UT, USA. 2ARUP Institute for Clinical and Experimental Pathology, Salt Lake City, UT, USA. 3Division of Hematology and Hematologic Malignancies, Department of Internal Medicine, University of Utah, Salt Lake City, UT, USA |
111 |
THE IMPACT OF NOVEL HEMOPHILIA TREATMENT PRODUCTS ON INHIBITOR TESTING FOR THE COMMUNITY COUNTS REGISTRY FOR BLEEDING DISORDERS SURVEILLANCE: AN UPDATE Amanda B. Payne, Connie H. Miller, Jennifer Driggers, Brian Boylan, Bonnie Werner, Glenn P. Niemeyer, Vanessa R. Byams, Karon Abe, Christopher J. Bean. National Center on Birth Defects and Developmental Disabilities, Centers for Disease Control and Prevention, Atlanta, GA, USA |
112 |
INTERIM SUBGROUP ANALYSIS OF HEMOPHILIA A SEVERITY ON THE EFFECTIVENESS AND SAFETY OF DAMOCTOCOG ALFA PEGOL FROM THE REAL-WORLD OBSERVATIONAL HEM-POWR STUDY Mark Reding1, Maria Teresa Alvarez Roman2, Martin Sanabria3, Giancarlo Castaman4, Maissaa Janbain5, Tadashi Matsushita6, Karina Meijer7, Kathrin Schmidt8, Johannes Oldenburg9. 1University of Minnesota Medical Center, Minneapolis, MN, USA. 2Hospital Universitario La Paz, Madrid, Spain. 3Bayer, Basel, Switzerland. 4Careggi University Hospital, Florence, Italy. 5Tulane School of Medicine, New Orleans, LA, USA. 6Nagoya University Hospital, Nagoya, Japan. 7University Medical Center Groningen, Groningen, Netherlands. 8Bayer, Berlin, Germany. 9University Clinic Bonn, Bonn, Germany |
113 |
A CASE OFLYMPHOMA-ASSOCIATEDACQUIREDVON WILLEBRAND SYNDROME RESPONSIVE TO SPLENECTOMY Natasha S. Rupani1, Fatima Khadadah1, Martina Trinkaus2, Jordan Scott1, Jerry Teitel3, Michelle Sholzberg4. 1Division of Hematology, Department of Medicine, University of Toronto, Toronto, ON, Canada. 2Division of Hematology/Oncology, Department of Medicine, University of Toronto, Toronto, ON, Canada. 3Division of Hematology, Department of Medicine, St. Michael's Hospital, University of Toronto, Toronto, ON, Canada. 4Division of Hematology/Oncology, Departments of Medicine and Laboratory Medicine a Pathobiology, St. Michael's Hospital, University of Toronto, Toronto, ON, Canada |
A7. PATHOPHYSIOLOGY OF THROMBOSIS |
114 |
THROMBO-INFLAMMATORY BIOMARKERS OF CARDIORENAL SYNDROME IN PATIENTS UNDERGOING MAINTENANCE HEMODIALYSIS IN END STAGE RENAL DISEASE Pranathi Karumanchi, Jawed Fareed, Vinod Bansal, Fakiha Siddiqui, Debra Hoppensteadt, Bulent Kantarcioglu. Loyola University Medical Center, Maywood, IL, USA |
A8. ANTITHROMBOTIC THERAPY |
115 |
DABIGATRAN REVERSAL WITH IDARUCIZUMAB IN A PEDIATRIC PATIENT AND SUMMARY OF THE CLINICAL STUDY IN ADULT PATIENTS WITH LOW BODY WEIGHTS ( Leonardo R. Brandao1, Joanne van Ryn2, Ildar Nurmeev3, Igor Tartakovsky2, Corinna Miede4, Charles V. Pollack Jr5, Manuella Albisetti6. 1The Hospital for Sick Children, Toronto, ON, Canada. 2Boehringer Ingelheim International GmbH, Ingelheim, Germany. 3Pediatric Hospital Kazan Medical University, Kazan, Russia. 4mainanalytics GmbH, Sulzbach/Taunus, Germany. 5University Mississippi School of Medicine, Jackson, MS, USA. 6University Children's Hospital, Zurich, Switzerland |
116 |
EFFECT OF THREE FACTOR XA INHIBITORS ON A SUBSET OF COMMON COAGULATION ASSAYS Ronda A Crist1, Daniel A Stephens1, George M Rodgers1, 2, 3, Karen A Moser1, 2, Kristi J Smock1, 2. 1ARUP Laboratories Institute for Clinical and Experimental Pathology, Salt Lake City, UT, USA. 2Department of Pathology, University of Utah School of Medicine, Salt Lake City, UT, USA. 3Division of Hematology, Department of Internal Medicine, University of Utah School of Medicine, Salt Lake City, UT, USA |
117 |
USP STANDARDIZED MIXTURES OF BOVINE, OVINE AND PORCINE HEPARIN EXHIBIT COMPARABLE BIOLOGIC EFFECTS TO REFERENCED SINGLE SOURCED HEPARINS AND MAY BE INTERCHANGEABLE Guy Olson, Walter Jeske, Omer Iqbal, Ambar Farooqui, Fakiha Siddiqui, Debra Hoppensteadt, Ahmed Kouta, Jawed Fareed. Loyola University Chicago - Cardiovascular Research Institute - Section of Hemostasis and Thrombosis, Maywood, IL, USA |
A9. INFORMATIONAL ABSTRACT (POSTER ONLY) |
118 |
HOW MEDICAL EXPERIENCES AND THOUGHTS OF PERSONS WITH INHERITED BLEEDING DISORDERS AND THEIR PARENTS/GUARDIANS ARE INFLUENCED BY THE CORONA PANDEMIC - AN INTERNATIONAL COMPARISON Maria E Santaella1, Michelle L Witkop1, Kate Khair2, Mabel Crescioni3, Cynthia Nichols1, Sylvia von Mackensen4. 1National Hemophilia Foundation, New York, NY, USA. 2The Haemophilia Society, London, United Kingdom. 3Hemophilia Federation of America, Washington, DC, USA. 4Department of Medical Psychology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany |
10:45 - 11:45 AM
SHORT TALKS
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SHORT TALKS - ANTICOAGULATION AND OTHER THERAPIES Chair/Organizer: Anna Parks, Julie Jaffray Sheraton Ballroom IV-V |
10:45 |
ADVERSE EVENTS IN LOW VERSUS NORMAL BODY WEIGHT PATIENTS PRESCRIBED APIXABAN OR RIVAROXABAN FOR ATRIAL FIBRILLATION. Deborah DeCamillo1, Brian Haymart1, Xiaowen Kong1, Scott Kaatz2, Mona Ali3, Geoffrey Barnes1, Scott Kaatz4. 1University of Michigan, Ann Arbor, MI, USA. 2Henry Ford Health System, Detroit, MI, USA. 3Beaumont Health, Royal Oak, MI, USA. 4Hurley Medical Center, Flint, MI, USA |
10:57 |
ANTI-FACTOR XA-BASED RISK STRATIFICATION FOR PATIENTS RECEIVING THERAPEUTIC ENOXAPARIN IS ASSOCIATED WITH INCREASED RISK OF RECURRENT/PROGRESSIVE THROMBOSIS AND HEMORRHAGE Emily C Drake1, Wallace Bourgeois1, 2, Juliann Duzan1, Nan Chen1, 2, Nikitha Ramesh1, Wendy B London1, 2, Riten Kumar1, 2. 1Boston Children's Hospital, Boston, MA, USA. 2Dana Farber Cancer Institute, Boston, MA, USA |
11:09 |
SAFETY OF THE CONCURRENT USE OF FOUR-FACTOR PROTHROMBIN COMPLEX CONCENTRATE WITH ANDEXANET ALFA FOR REVERSAL OF FACTOR XA INHIBITOR-RELATED BLEEDING: A RETROSPECTIVE CASE SERIES PARDIS NIAMI, PHARMD, AND TODD E. H. HECHT, MD, FACP, SFHM Pardis Niami, Todd Hecht. Hospital of the University of Pennsylvania, Philadelphia, PA, USA |
11:21 |
FOCUS GROUP-GUIDED DEVELOPMENT OF A NOVEL BLEEDING QUALITY OF LIFE PATIENT-REPORTED OUTCOME MEASURE FOR OLDER ADULTS Anna L. Parks1, Stacey L. Slager1, Margaret C. Fang2, Mark A. Supiano1, Patti P. Katz2, Daniel M. Witt1. 1University of Utah, Salt Lake City, UT, USA. 2University of California, San Francisco, San Francisco, CA, USA |
11:33 |
MANAGEMENT OF POTENTIAL DRUG-DRUG INTERACTIONS WITH NIRMATRELVIR-RITONAVIR AND ORAL ANTICOAGULANTS: A CASE SERIES Aaron S. Wilson1, Sara R. Vazquez1, 2, Daniel M. Witt1, 2. 1University of Utah College of Pharmacy Department of Pharmacotherapy, Salt Lake City, UT, USA. 2University of Utah Health Community Thrombosis Clinic, Salt Lake City, UT, USA |
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SHORT TALKS - BLEEDING I Chair/Organizer: Robert Sidonio, Yasmina Abajas Sheraton Ballroom I-III |
10:45 |
IMPACT OF ANEMIA ON VON WILLEBRAND FACTOR AND FACTOR VIII IN TYPE 1 VON WILLEBRAND DISEASE AND MILD HEMOPHILIA Maria E. Carter Febres, Cristina Tarango, Matthew Fenchel, Jennifer Pomales, Eric Mullins. Cincinnati Children's Hospital, Cincinnati, OH, USA |
10:57 |
PROPHYLAXIS WITH RECOMBINANT VON WILLEBRAND FACTOR IN PATIENTS WITH SEVERE VON WILLEBRAND DISEASE: PHASE 3 TRIAL RESULTS Frank W. G. Leebeek1, Flora Peyvandi2, Miguel Escobar3, Andreas Tiede4, Giancarlo Castaman5, Joan Gu6, Bjorn Mellgard7, Bruce Ewenstein7, Gulden Ozen7. 1Erasmus Medical Center, University Medical Center, Rotterdam, Netherlands. 2Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Fondazione IRCCS Ca, Milan, Italy. 3University of Texas Health Science Center at Houston, Houston, TX, USA. 4Hemostasis, Oncology and Stem Cell Transplantation, Hannover Medical School, Hannover, Germany. 5Center for Bleeding Disorders and Coagulation, Careggi University Hospital, Florence, Italy. 6Takeda Development Center Americas, Inc, Lexington, MA, USA. 7Takeda Development Center Americas, Inc, Cambridge, MA, USA |
11:09 |
INHIBITORS OF INORGANIC POLYPHOSPHATE AND NUCLEIC ACIDS LEAD TO DECREASED THROMBIN GENERATION IN TRAUMA PATIENTS Taleen A. MacArthur1, Julie Goswami1, Sreeparna Vappala 2, John Zietlow1, Stephanie A. Smith3, James H. Morrissey 3, Scott P. Zietlow1, Grant M. Spears1, Kent R. Bailey1, Jing-fei Dong4, Rosemary A. Kozar5, Jayachandran N. Kizhakkedathu 2, Myung S. Park1. 1Mayo Clinic, Rochester, MN, USA. 2University of British Columbia, Vancouver, BC, USA. 3University of Michigan School of Medicine , Ann Arbor, MI, USA. 4University of Washington School of Medicine, Seattle, WA, USA. 5Shock Trauma Center, University of Maryland School of Medicine, Baltimore, MD, USA |
11:21 |
EFANESOCTOCOG ALFA EXHIBITS VON WILLEBRAND FACTOR-INDEPENDENT PHARMACOKINETICS IN SEVERE HEMOPHILIA A: A POST HOC ANALYSIS FROM PHASE 1/2A STUDIES Janice/M. Staber1, Toshko/J. Lissitchkov2, Barbara/A. Konkle3, Amy/D. Shapiro4, Doris/V. Quon5, Roshni Kulkarni6, Melinda Hamilton7, Ekta/S. Chhabra8, Suresh Katragadda8, Arman Altincatal9, Annemieke Willemze10, Jennifer Dumont9, Margaret/V. Ragni11. 1University of Iowa Stead Family Children, Iowa City, IA, USA. 2Specialized Hospital for Active Treatment of Hematological Diseases, Department of Chemotherapy, Hemotherapy and Hereditary Blood Diseases at Clinical Hematology Clinic, Sofia Bulgaria. 3Washington Center for Bleeding Disorders and the University of Washington, Seattle, WA, USA. 4Indiana Hemophilia and Thrombosis Center, Indianapolis, IN, USA. 5Orthopaedic Hemophilia Treatment Center, Los Angeles, CA, USA. 6Michigan State University, East Lansing, MI, USA. 7Swedish Orphan Biovitrum AB, Stockholm Sweden. 8Sanofi, Waltham, MA, USA. 9Sanofi, Cambridge, MA, USA. 10Sanofi, Amsterdam, MA, Netherlands. 11Department of Medicine, University of Pittsburgh, and the Hemophilia Center of Western Pennsylvania, Pittsburgh, PA, USA |
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SHORT TALKS - LABORATORY ADVANCES Chair/Organizer: Andrew Goodwin , Cecily Allen Chicago Ballroom VII |
10:45 |
FACTOR VIII LEVELS AND INTERNATIONAL SOCIETY ON THROMBOSIS AND HEMOSTASIS (ISTH) DISSEMINATED INTRAVASCULAR COAGULATION (DIC) SCORES DO NOT DISCRIMINATE COAGULOPATHY OF LIVER DISEASE FROM DIC Cecily Allen1, Marina Heskel1, Ayesha Butt2, Alexander Pine2, Alfred Lee2. 1Yale School of Medicine, Dept. of Internal Medicine, New Haven, CT, USA. 2Yale School of Medicine, Dept. of Hematology, New Haven, CT, USA |
10:57 |
THE HEPARIN NEUTRALIZATION STEP OF ELISA CAN BE REDUNDANT FOR HEPARIN-INDUCED THROMBOCYTOPENIA (HIT) TESTING Xiangring He1, 2, Isabella K He3. 1University Hospitals of Cleveland, Cleveland, OH, USA. 2Case Western Reserve University, Cleveland, OH, USA. 3Northwestern University, Evanston, IL, USA |
11:09 |
DEVELOPMENT OF A MODIFIED BETHESDA ASSAY FOR DETERMINING THE PRESENCE OF ANTIDRUG ANTIBODIES TO EMICIZUMAB Hande Kizilocak1, Joshua Brown2, Desiree Tan-Castillo2, Guy Young1, 3. 1Children's Hospital Los Angeles, Hemostasis and Thrombosis Center, Los Angeles, CA, USA. 2Children, Los Angeles, CA, USA. 3University of Southern California, Keck School of Medicine, Los Angeles, CA, USA |
11:21 |
ANALYSIS OF GENETIC MUTATIONS AND FACTOR VIII ASSAY DISCREPANCY AMONG FEMALE CARRIERS OF HEMOPHILIA A Joanna M. Larson1, 2, Katherine E. Addy1, 2, Emma X. Li1, 2, John M. Hancock1, 2, 3, Natalie A. Montanez1, 2, Miguel A. Escobar1, 2, 3. 1Gulf States Hemophilia and Throbophilia Center, Houston, TX, USA. 2Department of Pediatrics, The University of Texas Health Science Center at Houston (UTHealth, Houston), Memorial Hermann, Texas Medical Center, Houston, TX, USA. 3Department of Internal Medicine, The University of Texas Health Science Center at Houston (UTHealth, Houston), Memorial Hermann, Texas Medical Center Houston, TX, Houston, TX, USA |
12:00 - 1:00 PM
SATELLITE SYMPOSIUM
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HELP CRACK THE CASE! A HEMOPHILIA A MYSTERY GAME AND AFTERNOON OF DISCUSSION (SPONSORED BY GENENTECH) Chicago Ballroom IX-X Genentech invites you to Help Crack the Case! in a fun-filled interactive mystery game showat this year's THSNA symposium. You'll hear from real patients and caregivers to find out just who's right for a subcutaneous prophylaxis option, and play along with our expert contestant, Dr. Michael Silvey. Throughout our game show, well explore considerations for identifying potential patients and learn more about the different patient types. You may be surprised at who these typical patients turn out to be! Plus, youll have an opportunity to have your questions answered in our live Q&A session. We look forward to seeing you there! |
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LONG-TERM MONITORING OF CLINICAL EFFICACY AND SAFETY PARAMETERS FOR INVESTIGATIONAL HEMOPHILIA GENE THERAPY (SPONSORED BY PFIZER) Chicago Ballroom VI This symposium will discuss the importance of patient monitoring both in the short- and long-term, exploring the variables that need to be considered in order to assess clinical efficacy and safety parameters of gene therapy. Presenters of this symposium will explore the practicalities of monitoring these parameters, focusing on coagulation assays and liver investigations, and review the questions that need to be addressed in the future in order to further our understanding of the mechanisms underlying this potential therapeutic approach. Gene therapy for the treatment of hemophilia is investigational. There are no gene therapies currently approved in the US for hemophilia. |
1:15 - 2:45 PM
THROMBOSIS / LABORATORY
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ECMO AND HEMOSTASIS Chair/Organizer: Nicole Zantek, Leo Brandao Chicago Ballroom VII |
1:15 |
ANTICOAGULATION MONITORING AND ANTITHROMBIN III SUPPLEMENTATION IN ECMO William Dager. University of California, Davis Medical Center |
1:40 |
ECMO AND PEDIATRICS Asavari Kamerkar. Children's Hospital Los Angeles |
2:05 |
UNDERSTANDING AND UTILIZATION OF TEG/ROTEM (THROMBOELASTROGRAPHY) Oksana Volod. Cedars Sinai |
2:30 |
Q&A. |
1:15 - 2:45 PM
BASIC SCIENCE
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PROCOAGULANT BIOLOGY IN SICKLE CELL DISEASE Chair/Organizer: Bryce Kerlin, Shannon Meeks Sheraton Ballroom IV-V |
1:15 |
ENDOTHELIAL THROMBIN - PAR1 SIGNALING AXIS IN SICKLE CELL DISEASE Rafal Pawlinski. University of North Carolina at Chapel Hill |
1:40 |
PLATELET-MEDIATED CONTRIBUTIONS TO HGB SS PATHOBIOLOGY Sruti Shiva. Universitoy of Pittsburgh |
2:05 |
EXTRACELLULAR VESICLES DISRUPT ENDOTHELIAL BARRIER FUNCTION IN SICKLE CELL Eric Beyer. University of Chicago |
2:30 |
Q&A. |
1:15 - 2:45 PM
HEMOSTASIS
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PSYCHOSOCIAL ASPECTS OF BLEEDING DISORDERS Chair/Organizer: Lena Volland, Michael Recht Sheraton Ballroom I-III |
INTRODUCTION VIDEO. |
1:15 |
IMPACT OF HEAVY MENSTRUAL BLEEDING AND BLOOD DISORDERS ON QUALITY OF LIFE Patricia Huguelet. University of Colorado School of Medicine and Children's Hospital Colorado |
1:40 |
HEMATOLOGIC ISSUES IN TRANSGENDER PATIENTS Joseph Shatzel. Cincinnati Children's Hospital Medical Center |
2:05 |
DEPRESSION AND SUICIDALITY IN BLEEDING DISORDER COMMUNITY Maria Iannone. Arizona Hemophilia and Thrombosis Center |
2:30 |
Q&A. |
2:45 - 3:45 PM
POSTERS/EXHIBITS/BREAK
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POSTERS/EXHIBITS/BREAK (click to view)
Riverwalk AB |
A1. ANTICOAGULATION CLINICS |
201 |
ADOPTION OF AN ELECTRONIC HEALTH RECORD TOOL TO PROMOTE VENOUS THROMBOEMBOLISM RISK ASSESSMENT FOR HOSPITAL MEDICINE PATIENTS Grace E. Eisenbiegler1, Katherine Wilkinson3, Rachel K. McEntee1, 2, Allen B. Repp1, 2, Neil A. Zakai1, 2, 3, Preetika Muthukrishnan1, 2. 1University of Vermont Medical Center, Burlington, VT, USA. 2Department of Medicine, University of Vermont Larner College of Medicine, Burlington, VT, USA. 3Department of Pathology and Laboratory Medicine Larner College of Medicine, Burlington, VT, USA |
A2. PLATELET ACTIVATION AND BIOCHEMISTRY |
202 |
DELETION OF MITOCHONDRIAL ENZYME PYRUVATE DEHYDROGENASE KINASES (PDK2 AND PDK4) INHIBITS PLATELET FUNCTION AND ARTERIAL THROMBOSIS Gagan D. Flora, Manasa K. Nayak, Madankumar Ghatge, Anil K. Chauhan. Division of Hematology/Oncology, University of Iowa, Iowa City, IA, USA |
A4. DISORDERS OF PLATELET NUMBER OR FUNCTION |
203 |
INFUSED HUMAN MEGAKARYOCYTES IN MICE SUPPORT A UNIQUE ROLE OF THE PULMONARY VASCULATURE IN THROMBOPOIESIS Hyunjun Kim1, Danuta Jarocha1, Ian Johnston1, Hyun Sook Ahn1, Deborah French1, Lubica Rauova1, 2, Mortimer Poncz1, 2. 1Children's Hospital of Philadelphia, Philadelphia, PA, USA. 2University of Pennsylvania, Philadelphia, PA, USA |
A5. BLOOD COAGULATION AND FIBRINOLYTIC FACTORS |
204 |
HEMOPHILIA A CARRIERS COMPARED WITH THE GENERAL FEMALE POPULATION: US ANALYSIS OF HEALTHCARE BURDEN Katharine Batt1, Maja Kuharic2, 3, Shan Xing3, Sepehr Farahbakhshian3, Jorge Caicedo3, Sreya Chakladar4, Riddhi Markan4, Michael Bullano3. 1Sprouts Consulting Ltd, Raleigh, NC, USA. 2Department of Pharmacy Systems, Outcomes and Policy, University of Illinois at Chicago, Chicago, IL, USA. 3Takeda Development Center Americas, Inc, Lexington, MA, USA. 4Complete HEOR Solutions, New Wales, PA, USA |
205 |
RISK FACTORS OF VENOUS THROMBOEMBOLISM IN ELDERLY PATIENTS WITH ACUTE LEUKEMIA Ambarina S. Faiz, Claire S. Philipp. Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USA |
206 |
HEPARIN ACTIVATION OF PROTEIN Z-DEPENDENT PROTEASE INHIBITOR (ZPI) ALLOSTERICALLY BLOCKS PROTEIN Z ACTIVATION THROUGH AN EXTENDED HEPARIN BINDING SITE Xin Huang, Richard Swanson, Steven T. Olson. University of Illinois Chicago, Chicago, IL, USA |
A6. DISORDERS OF COAGULATION OR FIBRINOLYSIS |
207 |
HEMOSTATIC EFFICACY OF RECOMBINANT FACTOR VII PRODUCT EPTACOG BETA FOR BLEEDING MANAGEMENT: REAL-WORLD EXPERIENCE OF PATIENTS WITH HEMOPHILIA A AND B WITH INHIBITORS Glaivy Batsuli1, Duc Q. Tran2, Guy Young3, Osman Khan4, Robert F. Sidonio1. 1Aflac Cancer and Blood Disorders Center of Children, Atlanta, GA, USA. 2Emory University, Hemophilia of Georgia Center for Bleeding and Clotting Disorders of Emory, Atlanta, GA, USA. 3Children, Los Angeles, CA, USA. 4University of Oklahoma Health Sciences Center, Oklahoma City, OK, USA |
208 |
REAL-WORLD EFFECTIVENESS OF DAMOCTOCOG ALFA PEGOL IN MILD AND MODERATE HEMOPHILIA A PATIENTS AGED 12 YEARS AND OLDER IN THE ATHNDATASET Martin Chandler1, Lena Charafi2, Thomas Moulton2, Michael Recht1. 1American Thrombosis a Hemostasis Network, Rochester, NY, USA. 2Bayer, Whippany, NJ, USA |
209 |
HEREDITARY FACTOR X DEFICIENCY BURDEN OF DISEASE AND IMPACT ON QUALITY OF LIFE IN PATIENTS AND CAREGIVERS: INTERIM FINDINGS FROM THE HEREDITARY FACTOR X DEFICIENCY IN AMERICA SURVEY Kim Clark1, Shirley P Huang2, Richard H Stanford2, Brian Branchford3, 4, 5. 1Bio Products Laboratory USA, Inc, Durham, NC, USA. 2AESARA, Inc, Chapel Hill, NC, USA. 3Versiti Blood Research Institute, Milwaukee, WI, USA. 4Medical College of Wisconsin, Milwaukee, WI, USA. 5Children, Milwaukee, WI, USA |
210 |
RIGHT ATRIAL THROMBUS INCIDENCE IN CHILDHOOD CANCER Sara McElroy, Lauren E. Amos, Emily Cramer, Michael Silvey, Joy M. Fulbright. Children's Mercy Hospital, Kansas City, MO, USA |
211 |
PERI-OPERATIVE ORTHOPEDIC MANAGEMENT OF A PATIENT WITH SEVERE HEMOPHILIA A AND A FACTOR VIII INHIBITOR ON EMICIZUMAB Natasha S. Rupani1, Roy Khalife2, Alan Tinmouth2, Sarah Ward3, Michelle Sholzberg4, Jerry Teitel5. 1Division of Hematology, Department of Medicine, University of Toronto, Toronto, ON, Canada. 2Division of Hematology, Department of Medicine, The Ottawa Hospital, University of Ottawa, Ottawa, ON, Canada. 3Division of Orthopaedic Surgery, Department of Surgery, St. Michael's Hospital, University of Toronto, Toronto, ON, Canada. 4Division of Hematology, Departments of Medicine and Laboratory Medicine a Pathobiology, St. Michael's Hospital, University of Toronto, Toronto, ON, Canada. 5Division of Hematology, Department of Medicine, St. Michael's Hospital, University of Toronto, Toronto, ON, Canada |
212 |
HETEROTOPIC OSSIFICATION IN HEMOPHILIA: AN UNANTICIPATED COMPLICATION FOLLOWING TRAUMATICALLY-INDUCED HEMATOMA Bruno U. K. Steiner1, 2, Mark A. Krimmel1, Eric Y. Chang 3, Merel A. Timmer4, Lorene E. Schmaderer5, Jeffrey Kallberg6, Jessica Ovans7, Grace Hernandez8, Jezzamine Choi1, Rebecca Kruse-Jarres1, 2. 1Washington Center for Bleeding Disorders, Seattle, WA, USA. 2University of Washington, Seattle, WA, USA. 3University of California, San Diego, San Diego, CA, USA. 4University Medicine Center Utrecht, Utrecht, Netherlands. 5Nebraska Medicine, Omaha, NE, USA. 6University of Texas Health Center San Antonio, San Antonio, TX, USA. 7Children's Minnesota, Minneapolis, MN, USA. 8The Center for Inherited Blood Disorders, Orange, CA |
A7. PATHOPHYSIOLOGY OF THROMBOSIS |
213 |
LEVELS OF HEPARIN INDUCED ANTI-PF4 ANTIBODIES AND ENDOGENOUS GLYCOSAMINOGLYCANS AND THEIR RELATIONSHIP WITH INFLAMMATORY BIOMARKERS IN PULMONARY EMBOLI PATIENTS. Bulent Kantarcioglu1, Roland Kraemer2, Fakiha Siddiqui1, Debra Hoppensteadt1, Walter Jeske1, Amir Darki1, Jawed Fareed1. 1Loyola University Medical Center, MAYWOOD, IL, USA. 2University of Heidelberg, Heidelberg Germany |
A8. ANTITHROMBOTIC THERAPY |
214 |
INTERMEDIATE VS. THERAPEUTIC DOSE ANTICOAGULATION IN HOSPITALIZED PATIENTS WITH COVID-19: RESULTS FROM A SINGLE ACADEMIC CENTER (THE IMPACT TRIAL) Maria T DeSancho1, Marina Loizou2. 1Weill Cornell Medicine, New York, NY, USA. 2Weill Cornell Medicine, New York, NY, USA |
215 |
POSTOPERATIVE ANTICOAGULATION STRATEGIES IN CHILDREN UNDERGOING INTERVENTION FOR CONGENITAL PORTOSYSTEMIC SHUNTS Abraham Haimed, Sherif Badawy, Caroline Lemoine, Riccardo Superina, Rukhmi Bhat. Ann and Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA |
216 |
ANTICOAGULATION QUALITY, EFFICACY, AND SAFETY OF EXTEMPORANEOUS LIQUID WARFARIN IN CHILDREN Hayley Hansen, Kelly Heilman, Yaser Diab. Children's National Hospital, Washington, DC, USA |
217 |
ENDOGENOUS HEPARIN LIKE GLYCOSAMINOGLYCAN IN VARIOUS DISEASES AS MEASURED BY A FLUORESCENCE QUENCHING METHOD Siddharth Mehrotra1, Joseph Lewis1, Fakiha Siddiqui1, Alfonso Tafur2, Bulent Kantarcioglu1, Debra Hoppensteadt1, Walter Jeske1, Jawed Fareed1, Roland Kraemer3. 1Loyola University Medical Center, MAYWOOD, IL, USA. 2North Shore Health Systems, Evanston, IL. 3University of Heidleberg, Heidelberg Germany |
A9. INFORMATIONAL ABSTRACT (POSTER ONLY) |
218 |
PREVALENCE AND RISK FACTORS FOR PULMONARY EMBOLISM IN CHILDREN WITH SICKLE CELL DISEASE: AN INSTITUTIONAL COHORT STUDY Natasha Bala, Stanek Joseph, Rodriguez Vilmarie, Villella Anthony. Nationwide Children's Hospital, Columbus, OH, USA |
3:45 - 5:15 PM
HEMOSTASIS / LABORATORY
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DIAGNOSIS AND MANAGEMENT OF VON WILLEBRAND DISEASE Chair/Organizer: Marian Rollins-Raval, Karen Moser Chicago Ballroom VII |
3:45 |
NEW RECOMMENDATIONS FOR DIAGNOSIS OF VWD FROM THE INTERNATIONAL GUIDELINES Robert Sidonio. Aflac Cancer and Blood Disorders and Emory University |
4:10 |
VWD IN WOMEN Maha Othman. Queen's University |
4:35 |
ACQUIRED VWD: DIAGNOSIS AND MANAGEMENT Kristi Smock. University of Utah and ARUP Laboratories |
5:00 |
Q&A. |
3:45 - 5:15 PM
BASIC SCIENCE
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INFLAMMATION AND HEMOSTASIS Chair/Organizer: Bryce Kerlin, Deirdre Nolfi-Donegan Sheraton Ballroom IV-V |
3:45 |
FIBRINOGEN AND S. AUREUS INFECTION Matthew Flick. University of North Carolina at Chapel Hill |
4:10 |
PLATELET-NEUTROPHIL CROSSTALK IN SYSTEMIC SCLEROSIS Roxane Darbousset. Boston children's hospital |
4:35 |
MECHANISMS LINKING FIBRINOGEN TO INFLAMMATORY COLITIS Joseph Palumbo. Cincinnati Children's Hospital Medical Center and The University of Cincinnati College of Medicine |
5:00 |
Q&A. |
3:45 - 5:15 PM
THROMBOSIS
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THE CHANGING ROLE OF THE ANTICOAGULATION SERVICE Chair/Organizer: Vinai Bhagirath, Gary Woods Sheraton Ballroom I-III |
3:45 |
ARE ANTICOAGULATION CLINICS THE NEXT MEDICAL DINOSAUR? Elizabeth Renner. Michigan Medicine |
4:10 |
ANTICOAGULATION AND PEDIATRICS: CONSIDERATIONS ACROSS CARE SETTINGS Jennifer Meldau. Childrens National Hospital |
4:35 |
ANTICOAGULATION MODELS OF CARE IN THE INPATIENT SETTING Gary Woods. Children's Healthcare of Atlanta and Emory University |
5:00 |
Q&A. |
5:15 - 6:00 PM
POSTERS/EXHIBITS/BREAK
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POSTERS/EXHIBITS/BREAK (click to view)
Riverwalk AB |
A1. ANTICOAGULATION CLINICS |
301 |
EVALUATION OF CARE FOR PATIENTS WITH ANTIPHOSPHOLIPID SYNDROME AT AN ANTICOAGULATION MANAGEMENT CLINIC “CAPS-AMC” Jennifer Pitman1, 2, Alison Bond1, 2, Barbara Huth1, Rita Selby1, 2, William Geerts1, 2. 1Sunnybrook Health Sciences Centre, Toronto, ON, Canada. 2University of Toronto, Toronto, ON, Canada |
A2. PLATELET ACTIVATION AND BIOCHEMISTRY |
302 |
DIRECT INHIBITION OF THE Gα13-P115RHOGEF INTERACTION BY THE INTEGRIN β3 SUBUNIT AND ITS ROLE IN REGULATING EXOCYTOSIS IN PLATELETS. Yaping Zhang, Xiaojuan Zhao, Bo Shen, yanyan Bai, Claire Chang, Aleksandra Stojanovic, Randal A Skidgel, Ni Cheng, Xiaoping Du. 1Department of Pharmacology and Regenerative Medicine, University of Illinois at Chicago, chicago, IL, USA |
A4. DISORDERS OF PLATELET NUMBER OR FUNCTION |
303 |
VALIDATION OF A NOVEL ADAMTS13 ASSAY FOR CHARACTERIZATION OF PATIENTS WITH THROMBOTIC THROMBOCYTOPENIC PURPURA J. Cameron Barton, Frida Miranda, Cooper Anderson, Joshua Muia. Oklahoma State University Center for Health Sciences, Tulsa, OK, USA |
A5. BLOOD COAGULATION AND FIBRINOLYTIC FACTORS |
304 |
THROMBOMODULIN SENSITIVITY DECREASES IN THROMBIN GENERATION ASSAYS IN THE EARLY POSTPARTUM PERIOD Maria Cristina Bravo1, Kelley C McLean2, Matthew T Gissel1, Ira M Bernstein2, Thomas Orfeo1. 1University of Vermont, Department of Biochemistry, Colchester, VT, USA. 2University of Vermont Medical Center, Department of Obstetrics, Gynecology, And Reproductive Sciences, Burlington, VT, USA |
305 |
PLASMINOGEN REPLACEMENT THERAPY FOR THE TREATMENT OF PATIENTS WITH CONGENITAL PLASMINOGEN DEFICIENCY: RESULTS FROM THE PHASE 2/3 STUDY Amy D Shapiro1, Per M Sandset2, Joseph M Parker3, Karen Thibaudeau4, Prasad Mathew4, 5, Erin Weigel6, Charles Nakar1. 1Indiana Hemophilia a Thrombosis Center, Inc, Indianapolis, IN, USA. 2Oslo University Hospital, Oslo, Norway. 3Prometic/Liminal Biosciences Inc, Laval, QC, Canada. 4Global Medical AffairsKedrion SpA, Lucca, Italy. 5Presbyterian Hospital, Albuquerque, NM, USA. 6Kedrion BioPharma, Fort Lee, NJ, USA |
A6. DISORDERS OF COAGULATION OR FIBRINOLYSIS |
306 |
COMPARISON OF INFLAMMATORY BIOMARKERS BETWEEN SARS-COV-2 VACCINATED AND UNVACCINATED SUBJECTS Nusrat Jabeen1, Anusha Amanullah2, Mushtaq Hussain2, Bulent Kantarcioglu1, Fakiha Siddiqui1, Jawed Fareed1. 1University of Karachi, Department of Microbiology, Karachi Pakistan. 2Dow University of health Sciences, Dow College of Biotechnology, Karachi Pakistan. 3Loyola University Medical Center, Maywood, IL, USA |
307 |
PHASE 3 STUDY TO INVESTIGATE THE EFFICACY, PHARMACOKINETICS, IMMUNOGENICITY AND SAFETY OF VON WILLEBRAND FACTOR/FACTOR VIII CONCENTRATE IN PATIENTS WITH SEVERE VON WILLEBRAND DISEASE UNDER 6 YEARS OF AGE Akshat Jain1, Tarja-Elina Weisz2, Cristina Solomon3, Sylvia Werner2. 1Loma Linda University School of Medicine, Loma Linda, CA, USA. 2Octapharma Pharmazeutika Produktionsges. m. b. H, Vienna, Austria. 3Octapharma AG, Lachen Switzerland |
308 |
THROMBOTIC COMPLICATIONS IN PATIENTS WITH FACTOR V LEIDEN AND COVID-19: INSIGHTS FROM THE CORONA-VTE NETWORK Candrika D. Khairani1, 2, Galit Frydman3, Barry Berger3, Rachel P. Rosovsky4, Antoine Bejjani1, 2, Nicole Porio1, 2, Samuel Z. Goldhaber1, 2, Gregory Piazza1, 2. 1Thrombosis Research Group, Brigham and Women, Boston, MA, USA. 2Cardiovascular Medicine Division, Brigham and Women, Boston, MA, USA. 3Coagulo Medical Technologies, Inc, Auburndale, MA, USA. 4Division of Hematology/Oncology, Massachusetts General Hospital, Harvard Medical School, Boston, MA, USA |
309 |
POST-MARKETING OBSERVATIONAL STUDY OF THE SAFETY AND EFFICACY OF FIBRINOGEN CONCENTRATE IN CONGENITAL FIBRINOGEN DEFICIENCY IN PATIENTS OF ALL AGES Flora Peyvandi1, 2, Gita Pezeshki3, Cristina Solomon4, Sylvia Werner3. 1Fondazione IRCCS Ca, Milan, Italy. 2Department of Pathophysiology and Transplantation, Universita degli Studi di Milano, Milan, Italy. 3Octapharma USA, Paramus, NJ, USA. 4Octapharma AG, Lachen, Switzerland |
310 |
GENETICS INFLUENCE THE ABILITY TO FORM NEUTRALIZING ANTIBODIES TO FACTOR VIII THROUGH A GERMINAL CENTER RESPONSE Seema R Patel1, Taran Lundgren1, 2, Wallace Hunter Baldwin1, Courtney Cox1, Ernest T Parker1, Ryan P Jajosky3, Patricia E Zerra1, 4, Cassandra Josephson1, Christopher Doering1, Sean R Stowell3, Shannon L Meeks1. 1Aflac Cancer and Blood Disorders Center, Children, Atlanta, GA, USA. 2Graduate Program in Molecular and Systems Pharmacology, Laney Graduate School, Emory University School of Medicine, Atlanta, GA, USA. 3Brigham and Women, Boston, MA, USA. 4Center for Transfusion Medicine and Cellular Therapies, Department of Laboratory Medicine and Pathology, Emory University School of Medicine, Atlanta, GA, USA |
311 |
REAL-WORLD EFFECTIVENESS OF OCTOCOG ALFA TO TREAT HEMOPHILIA A IN JAPAN AND THE UNITED STATES Michael Recht1, Ei Kinai2, Masashi Taki3, Sayaka Tachikawa4, Ryan Farej5, Thomas Moulton5, Midori Shima6, Martin Chandler1, Katsuyuki Fukutake2, 7. 1American Thrombosis a Hemostasis Network, Rochester, NY, USA. 2Department of Laboratory Medicine, Tokyo Medical University, Tokyo, Japan. 3Department of Pediatrics, St. Marianna University School of Medicine, Kawasaki City, Japan. 4Bayer Yakuhin, Ltd, Osaka, Japan. 5Bayer U. S. LLC, Whippany, NJ, USA. 6Department of Pediatrics, Nara Medical University, Nara, Japan. 7Department of Blood Coagulation, Ogikubo Hospital, Suginami City, Japan |
312 |
SUCCESSFUL USE OF EPTACOG BETA PROPHYLAXIS IN AN ADOLESCENT WITH SEVERE HEMOPHILIA B WITH HIGH-TITER INHIBITOR RESULTING IN DECREASED BLEEDING EPISODES AND COST OF TREATMENT Kimberley Youkhana, Yasmina Abajas. University of North Carolina Blood Research Center, Chapel Hill, NC, USA |
313 |
LONGITUDINAL EFFICACY AND SAFETY OF N9-GP FOR PROPHYLAXIS AND BLEED CONTROL IN US PATIENTS Guy Young1, Miguel Escobar2, Ayesha Zia3, Pernille Hojlund Nielsen4, Adam R Wufsus5, Laura Sedita Alaimo5, Allison P Wheeler6. 1University of Southern California Keck School of Medicine, Los Angeles, CA, USA. 2University of Texas Health Science Center, Houston, TX, USA. 3UT Southwestern Medical Center, Dallas, TX, USA. 4Novo Nordisk A/S, Soborg, Denmark. 5Novo Nordisk Inc, Plainsboro, NJ, USA. 6Vanderbilt University Medical Center, Vanderbilt University, Nashville, TN, USA |
A7. PATHOPHYSIOLOGY OF THROMBOSIS |
314 |
FEW PATIENTS WITH LIVEDOID VASCULOPATHY DEMONSTRATE COMPLEMENT DYSREGULATION IN A FUNCTIONAL ASSAY Harish Eswaran1, Shruti Chaturvedi2, Paul Googe3, Gloria Gerber2, Xiang-Zuo Pan2, Robert Brodsky2, Stephan Moll4. 1Department of Medicine, University of North Carolina School of Medicine, Chapel Hill, NC, USA. 2Division of Hematology, Department of Medicine, Johns Hopkins University School of Medicine, Baltimore, MD, USA. 3Department of Dermatology, University of North Carolina School of Medicine, Chapel Hill, NC, USA. 4Division of Hematology, Department of Medicine, University of North Carolina School of Medicine, Chapel Hill, NC, USA |
A8. ANTITHROMBOTIC THERAPY |
315 |
MEDICATION LIST ACCURACY AND GUIDELINE CONCORDANCE OF PRIMARY PREVENTION ASPIRIN USE Naina Chipalkatti1, Geoff Barnes2, Linda Bashaw1, Adam Davie1, Jennifer Griggs3, Molly Harrod4, Jacob Kurlander5, Christine Medaugh6, Rebeca Packard7, Suman Sood3, Liz Spranger1, Sarah Vordenberg8, Jordan Schaefer3. 1Department of Internal Medicine, University of Michigan, Ann Arbor, MI, USA. 2Department of Internal Medicine, Division of Cardiology, University of Michigan, Ann Arbor, MI, USA. 3Department of Internal Medicine, Division of Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA. 4Center for Clinical Management Research, VA Ann Arbor Healthcare System, Ann Arbor, MI, USA. 5Department of Internal Medicine, Division of Gastroenterology, University of Michigan, Ann Arbor, MI, USA. 6Department of Family Medicine, University of Michigan, Ann Arbor, MI, USA. 7Health Information Technology a Services, University of Michigan, Ann Arbor, MI, USA. 8College of Pharmacy, University of Michigan, Ann Arbor, MI, USA |
316 |
TISSUE FACTOR PATHWAY INHIBITOR (TFPI) RELEASE BY BOVINE, OVINE, PORCINE UNFRACTIONATED HEPARINS AND SULODEXIDE IN PRIMATES. Jawed Fareed1, Ahmed Kouta1, Emily Bontekoe1, Richard Duff1, Walter Jeske1, Debra Hoppensteadt1, Mark Jaradeh1, Yiming Yao2, Guy Olson1. 1Loyola University Medical Center, Maywood, IL, USA. 2Ronnsi Pharma, Suzhou China |
317 |
AUTOMATED THROMBIN GENERATION ASSAY PERFORMANCE IN PEDIATRIC PATIENTS TREATED WITH VARIABLE ANTICOAGULANTS: A PILOT STUDY. Vadim Kostousov, Karen Bruzdoski, Amir Navaei, Lisa Hensch, Shiu-Ki Hui, Jun Teruya. Texas Children's Hospital, Houston, TX, USA |
A9. INFORMATIONAL ABSTRACT (POSTER ONLY) |
318 |
NATIONAL ECONOMIC BURDEN OF ADULTS WITH SEVERE HEMOPHILIA A MANAGED WITH PROPHYLAXIS IN THE UNITED STATES Taiji Wang1, Er Chen2, Catherine Regan3, Keziah Cook1, Noam Kirson4, Edmund Pezalla5, Mark Skinner6, 7. 1Analysis Group Inc, Menlo Park, CA, USA. 2BioMarin Pharmaceutical Inc, Novato, CA, USA. 3Analysis Group Inc, San Francisco, CA, USA. 4Analysis Group Inc, Boston, MA, USA. 5Enlightenment Bioconsult, LLC, Daytona Beach, FL, USA. 6Institute for Policy Advancement Ltd, Washington DC United States. 7McMaster University, Hamilton, ON, USA |
6:00 - 7:15 PM
SATELLITE SYMPOSIUM
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2022 DINNER SYMPOSIUM: ADVANCING NEW FRONTIERS IN HEMOPHILIA MANAGEMENT (SPONSORED BY BIOMARIN PHARMACEUTICAL INC. ) Chicago Ballroom IX-X Recognizing the history and reasoning for exploring gene therapy in lifelong conditions like hemophilia will be a focus of this conversation with the experts. During this dinner symposium, attendees will be part of expert discussions on topics relating to liver health in the context of liver-directed gene therapy, follow-up care and surveillance registries in patients with hemophilia, and practical logistics for establishing and maintaining successful gene therapy transfer clinic operations. The four leading experts will provide updates on these cutting-edge, scientific topics followed by an open panel discussion with attendees. We hope that you will join us. |
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THE FIRST AND ONLY FDA-APPROVED AGENT FOR REVERSAL OF FXA INHIBITOR ACTIVITY IN PATIENTS WITH LIFE-THREATENING OR UNCONTROLLED BLEEDING (SPONSORED BY ASTRAZENECA) Chicago Ballroom VI This program will discuss the burden of life-threatening bleeds related to FXa inhibitors, and focus on the mechanism of action, efficacy, and safety of a reversal agent indicated for patients treated with anticoagulants who have life-threatening bleeding. |
7:30 - 9:30 PM
POSTER SESSION
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VIRTUAL POSTERS (ON-DEMAND ONLY) Virtual Meeting System |
RIVAROXABAN FOR THROMBOSIS IN PEDIATRIC PATIENTS: A RETROSPECTIVE OBSERVATIONAL STUDY FROM THE LOW/MIDDLE INCOME SETTING. Aimen Mehmood, Bushra Moiz, Zehra Fadoo, Asim Belgaumi, Naureen Mushtaq, Sadaf Altaf. Aga Khan University, Karachi, Pakistan |
“DOES MY PATIENT HAVE HEPARIN-INDUCED THROMBOCYTOPENIA? THERE SHOULD BE AN APP FOR THAT. ” Frederic Allemand, Matthieu Stoll. Emosis, Illkirch-Graffenstaden, France |
SURVIVAL OUTCOMES FOLLOWING INFERIOR VENA CAVA FILTER INSERTION IN CANCER PATIENTS; A COMPREHENSIVE CANCER CENTER EXPERIENCE. Hikmat Abdel-Razeq1, Faris Tamimi1, Rashid Abdel-Razeq1, Ahmad Naser1, Rama Al Masri2, Jaafar Bani Issa1, Baha' Sharaf1, Osama Salama1, Rayan Bater1. 1King Hussein Cancer Center, Amman, Jordan. 2Istishari Hospital, Amman, Jordan |
CHARACTERIZING RE-ADMISSION, BLEEDING, AND THROMBOTIC EVENTS IN COVID-19 PATIENTS RECEIVING ANTICOAGULATION THERAPY: A SINGLE-INSTITUTION RETROSPECTIVE ANALYSIS Tony Zhuang1, Rachel Mather1, Smitha John2, Judy Gichoya1, Alyssa Utz1, Mikhail Akbashev1. 1Emory University School of Medicine, Atlanta, GA, USA. 2Morehouse School of Medicine, Atlanta, GA, USA |
A RETROSPECTIVE REVIEW OF INFERIOR VENA CAVA (IVC) FILTER USE Yuxin Bai1, Stephanie Fontyn1, Samantha Bolger1, Kaity Greco1, Caroline Hamm1, 2, Andrea Cervi1, 2. 1Schulich School of Medicine a Dentistry, London, ON, Canada. 2Department of Medical Oncology, Windsor Regional Cancer Center, Windsor, ON, Canada |
THROMBOELASTOGRAPHY TRIGGERED BY CONTACT PATHWAY ACTIVATION REQUIRES PLATELET INTEGRIN ACTIVATION AND CONTRACTION BUT NOT MAJOR PLATELET SIGNALING PATHWAYS Tanvi Rudran, Robert H Lee, Silvio Antoniak, Alisa S Wolberg, Wolfgang Bergmeier. University of North Carolina, Chapel Hill, NC, USA |
ALTERATIONS IN THE PLATELET COUNT AND MORTALITY DUE TO COVID-19 DURING THE FIRST AND SECOND WAVE IN PERUVIANS: A RETROSPECTIVE COHORT IN A NATIONAL REFERENCE CENTER. Rafael Pichardo-Rodriguez1, Willy Pena-Oscuvilca2, Oscar Ruiz-Franco2, Fausto Garmendia-Lorena2. 1Research Institute in Biomedical Sciences (INICIB). Ricardo Palma University, Lima, Peru. 2Clinical Research Institute, Lima, Peru |
PROFILING OF THROMBOINFLAMMATORY BIOMARKERS: A DEPICTION OF THE ENDOTHELIAL PATHOGENESIS OF ATRIAL FIBRILLATION Gabriel Dungan1, Ameer Odeh1, Emily Bontekoe1, Fakiha Siddiqui1, Debra Hoppensteadt1, Omer Iqbal1, Jawed Fareed1, Guy Olson1, Mushabbar Syed2. 1Loyola University Medical Center, Department of Pathology and Laboratory Medicine, Maywood, IL, USA. 2Loyola University Medical Center, Department of Cardiology, Maywood, IL, USA |
GENERATION OF ANTICOAGULANT RNA APTAMERS TARGETING COFACTORS THAT INHIBIT CLOTTING IN NORMAL AND COVID-19 PATIENT SAMPLES Haixiang Yu1, Erin Soule1, Lyra Olson1, Ibtehaj Naqvi1, Shekhar Kumar2, Juliana Layzer1, Sriram Krishnaswamy2, Bruce Sullenger1. 1Duke University, Department of Surgery, Durham, NC, USA. 2Children, Philadelphia, PA, USA |
REDUCED TIME TO GASTROINTESTINAL PROCEDURE AFTER WARFARIN REVERSAL WITH FOUR FACTOR PROTHROMBIN COMPLEX CONCENTRATE (4F-PCC) AS COMPARED TO PLASMA IN PATIENTS WITH GASTROINTESTINAL BLEEDING Hannah L McRae1, Hannah Spector1, Tanzy Love2, Deborah Sturpe3, Kalynn Northam4, Majed A Refaai1. 1Department of Pathology and Laboratory Medicine, Transfusion Medicine Division, University of Rochester Medical Center, Rochester, NY, USA. 2Department of Biostatistics and Computational Biology, University of Rochester Medical Center, Rochester, NY, USA. 3Division of Pharmacotherapy and Experimental Therapeutics, University of North Carolina Eshelman School of Pharmacy, Chapel Hill, NC, USA. 4Department of Pharmacy, University of North Carolina Medical Center, Chapel Hill, NC, USA |
ONCE DAILY DOSING OF PROTEIN C CONCENTRATE FOR SEVERE PROTEIN C DEFICIENCY Melissa Verdolotti, Montcrieff Caitlin. Rhode Island Hemostasis a Thrombosis Center, Providence, RI, USA |
EVALUATING THE ROLE OF ROTATIONAL THROMBOELASTOMETRY (ROTEM) AS A PREDICTOR FOR POSTPARTUM HEMORRHAGE Radia Ksayer, Karam Zakharia, Cindy Leissinger, Maissaa Janbain. Tulane University, New Orleans, LA, USA |
SINGLE-NUCLEOTIDE POLYMORPHISMS IN THE ABO BLOOD GROUP LOCUS ARE PLEIOTROPICALLY ASSOCIATED WITH THE PLASMA LEVELS OF FACTOR VIII COAGULANT ACTIVITY AND VON WILLEBRAND FACTOR ANTIGEN IN MEXICAN AMERICANS OF SOUTH TEXAS Shuchita Jhaveri1, Vincent P. Diego2, 3, Marcio A. Almeida2, 3, Hoang A. Nguyen1, Juan M. Peralta2, 3, Joanne E. Curran2, 3, Donna Lehman4, Ralph DeFronzo4, Miguel A. Escobar5, Raja Rajalingam6, Jerry S. Powell7, 8, Sarah Williams-Blangero2, 3, Ravindranath Duggirala2, 3, John Blangero2, 3, Tom Howard2, 3, 7, 9. 1University of Texas Rio Grande Valley (UTRGV) School of Medicine (SOM), Edinburg, TX, USA. 2Department of Human Genetics, UTRGV SOM, Brownsville, TX, USA. 3South Texas Diabetes and Obesity Institute, UTRGV SOM, Brownsville, TX, USA. 4University of Texas Health Science Center at San Antonio SOM, San Antonio, TX, USA. 5Division of Hematology and Oncology, Department of Internal Medicine, McGovern SOM, University of Texas Health Science Center at Houston, Houston, TX, USA. 6Immunogenetics and Transplantation Laboratory, Department of Surgery, School of Medicine, University of California at San Francisco, San Francisco, CA, USA. 7Haplogenics Corporation, Brownsville, TX, USA. 8Division of Hematology and Oncology, Department of Medicine, SOM, University of California at Davis, Davis, CA, USA. 9Department of Pathology and Laboratory Medicine, VA Texas Valley Coastal Bend Health Care System, Harlingen, TX, USA |
FABRICATION OF A PHYSIOLOGICALLY RELEVANT FLUORESCENTLY LABELED CLOT IN A CHANDLER LOOP Ziqian Zeng1, Alexei Christodoulides2, Nathan J Alves1, 2. 1Purdue University - Department of Biomedical Engineering, West Lafayette, IN, USA. 2Indiana University School of Medicine - Department of Emergency Medicine, Indianapolis, IN, USA |
FACTOR VII ACTIVATING PROTEASE DOES NOT PREDICT THE DISABILITY OF ISCHEMIC STROKE PATIENTS Artur Slomka1, Iga Kwiatkowska1, Malgorzata Wiszniewska2, Ewa Zekanowska1. 1Department of Pathophysiology, Nicolaus Copernicus University in Torun, Ludwik Rydygier Collegium Medicum, Bydgoszcz, Poland. 2Stanislaw Staszic Specialist Hospital, Neurology and Stroke Care Unit, Pila, Poland |
HEMOSTASIS DISORDERS AND CORONAVIRUS DISEASE: EXPERIENCE OF THE HEMATOLOGY LABORATORY OF CHU IBN ROCHD OF CASABLANCA Chaimaa Zirhi1, Hanaa Bencharef2, Bouchra Ifegh3, Bouchra Oukkache4. 1Hematology Laboratory, CHU Ibn Rochd Casablanca, Casablanca, Morocco. 2Faculty of Medicine and Pharmacy of Casablanca, Hassan II University, Casablanca, Morocco. 3Hematology Laboratory, CHU Ibn Rochd Casablanca, Casablanca, Morocco. 4Faculty of Medicine and Pharmacy of Casablanca, Hassan II University, Casablanca, Morocco |
CHARACTERISTICS AND HEALTH CARE UTILIZATION AMONG PERSONS WITH INHERITED BLEEDING DISORDERS RECEIVING CARE OUTSIDE OF US HEMOPHILIA TREATMENT CENTERS: A COLLABORATION BETWEEN THE CENTERS FOR DISEASE CONTROL AND PREVENTION AND TWO ACADEMIC MEDICAL CENTERS Courtney D. Thornburg1, 2, Binh Le3, Vanessa R. Byams3, Meredith Oakley3, Kristin Byrne4, Ara Metjian5. 1Rady Children's Hospital San Diego, San Diego, CA, USA. 2UC San Diego, La Jolla, CA, USA. 3National Center on Birth Defects and Developmental Disabilities, Division of Blood Disorders, Centers for Disease Control and Prevention, Atlanta, GA, USA. 4Duke University Health System, Durham, NC, USA. 5University of Colorado Anschutz Medical Center, Denver, CO, USA |
ACQUIRED FACTOR XIII DEFICIENCY DETERMINES POSTOPERATIVE BLOOD LOSS Emilie K. von Depka1, Carsten Detering1, Michael Boeker2, Mario von Depka1. 1Werlhof Institute, Hannover, Germany. 2Paracelsus Klinik am Silbersee, Langenhagen, Germany |
SHARED DECISION-MAKING FOR HEMOPHILIA GENE THERAPY: PATIENT PERSPECTIVES AND EXPECTATIONS Jacqueline Limjoco1, Hannah Reyes1, Jennifer Han1, 2, Courtney Thornburg1, 2. 1Rady Children's Hospital San Diego, San Diego, CA, USA. 2UC San Diego School of Medicine, La Jolla, CA, USA |
LIGHT-CHAIN PARAPROTEINS IN COAGULATION ASSAYS AND THEIR CLINICAL ASSOCIATIONS: A REPORT OF 6 CASES Jing Jin1, Steven Baker2, James Zehnder3. 1Department of Special Coagulation, Clinical Laboratories, Stanford Health Care, Palo Alto, CA, USA. 2Department of Pathology, University of Utah, Salt Lake city, UT, USA. 3Department of Pathology, School of Medicine, Stanford University, Stanford, CA, USA |
THE ORIGIN OF FERRITIN REFERENCE INTERVALS: A SYSTEMATIC REVIEW Judy Truong1, Kanza Naveed1, Daniel Beriault2, 3, David Lightfoot4, Michael Fralick5, Michelle Sholzberg6, 7, 8, 9. 1Temerty Faculty of Medicine, University of Toronto, Toronto, ON, Canada. 2Division Head, Clinical Biochemistry, Department of Laboratory Medicine, St. Michael, Toronto, ON, Canada. 3Assistant Professor, Department of Laboratory Medicine and Pathobiology, University of Toronto, Toronto, ON, Canada. 4Information Specialist, Health Sciences Library, St. Michael's Hospital, Toronto, ON, Canada. 5Clinician Scientist, Lenenfeld-Tanenbaum Research Institute, Sinai Health, Toronto, ON, Canada. 6Head of the Division of Hematology-Oncology, St. Michael, Toronto, ON, Canada. 7Director of the Hematology-Oncology Clinical Research Group, St. Michael, Toronto, ON, Canada. 8Assistant Professor, University of Toronto, Toronto, ON, Canada. 9Associate Scientist, Li Ka Shing Knowledge Institute, Toronto, ON, Canada |
THE ROLE OF EMICIZUMAB IN BLEED CONTROL IN PATIENTS WITH AQUIERED HEMOP0HILIA A Karam Zakharia, Radia Ksayer, Cindy leissinger, Maissaa Janbain. Tulane University, New Orleans, LA, USA |
SYNONYMOUS ADAMTS13 VARIANTS IMPACT MOLECULAR CHARACTERISTICS AND CONTRIBUTE TO VARIABILITY IN ACTIVE PROTEIN ABUNDANCE Katarzyna /I Jankowska, Douglas Meyer, David /D Holcomb, Jacob Kames, Nobuko Katagiri, Chava Kimchi-Sarfaty. US Food and Drug Administration, Silver Spring, MD, USA |
THE IMPACT OF OBESITY ON CHRONIC PAIN IN PATIENTS WITH HEMOPHILIA: A MULTICENTER RETROSPECTIVE ANALYSIS Keerthy Joseph1, Adam Cuker2, 3, Skye Peltier4, Mark Reding5, Xiaoyan Han6, Allyson Pishko2. 1Department of Medicine, Mercy Catholic Medical Center, Darby, PA, USA. 2Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA. 3Department of Pathology and Laboratory Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA. 4American Thrombosis and Hemostasis Network, Rochester, NY, USA. 5Center for Bleeding and Clotting Disorders, University of Minnesota, Minneapolis, MN, USA. 6Department of Biostatistics, Epidemiology and Informatics (DBEI), Perelman School of Medicine, University of Pennsylvania, Philadlephia, PA, USA |
ONCE-WEEKLY ADMINISTRATION OF NONACOG BETA PEGOL(N9-GP) IS ASSOCIATED WITH HIGH TREATMENT ADHERENCE AND REDUCTIONS IN ANNUALIZED BLEEDING RATES IN CHILDREN WITH HEMOPHILIA B Manuel Carcao 1, Susan Kearney2, Allison Wheeler3, Chunduo Shen4, Helle Holst4, Ayesha Zia5. 1Division of Hematology/Oncology, Hospital for Sick Children, Toronto, ON, Canada. 2Center for Bleeding and Clotting Disorders, Children, Minneapolis, MN, USA. 3Vanderbilt University Medical Center, Nashville, TN, USA. 4Novo Nordisk, Copenhagen, Capital region, Denmark. 5Division of Hematology/Oncology, University of Texas Southwestern Medical Center, Dallas, TX, USA |
NEUROCOGNITIVE AND NEUROLOGICAL OUTCOMES IN CHILDREN WITH HEMOPHILIA B ARE UNAFFECTED BY LONG-TERM EXPOSURE TO NONACOG BETA PEGOL (N9-GP) Manuel Carcao1, Anthony KC Chan2, Allison P Wheeler3, Pernille Hojlund Nielsen4, Helle Holst4. 1Division of Hematology/Oncology, Department of Pediatrics, Hospital for Sick Children, Toronto, ON, Canada. 2Department of Pediatrics, McMaster Children's Hospital, McMaster University, Hamilton, ON, Canada. 3Vanderbilt University Medical Center, Nashville, TN, USA. 4Novo Nordisk A/S, Copenhagen, Capital region, Denmark |
CLINICAL OUTCOMES OF COVID-19 IN PATIENTS WITH VON WILLEBRAND DISEASE: A MULTICENTER DATABASE STUDY Meric Mericliler1, 2, Ruchi Desai1, 2. 1Division of Hematology and Oncology, Virginia Commonwealth University, Richmond, VA, USA. 2Massey Cancer Center, Virginia Commonwealth University, Richmond, VA, USA |
FIRST NEUTRALIZING ANTIDRUG ANTIBODY TO EMICIZUMAB IN A PATIENT WITH SEVERE HEMOPHILIA A WITHOUT INHIBITORS Michael F. Guerrera1, Hande Kizilocak2, Carly Varela1, 3, Christine Guelcher1, Lauren Godby3, Guy Young2. 1Children's National Hospital, Washington, DC, USA. 2Children's Hospital Los Angeles, Los Angeles, CA, USA. 3Pediatric Specialists of Virginia, Fairfax, VA, USA |
CONTEMPORARY MANAGEMENT OF PREGNANT WOMEN WITH TYPE 1 VON WILLEBRAND DISEASE: A SINGLE-INSTITUTION RETROSPECTIVE STUDY Ming Y Lim1, George M Rodgers1, Sara E Simonsen2. 1University of Utah Health, Salt Lake City, UT, USA. 2University of Utah College of Nursing, Salt Lake City, UT, USA |
IMPACT OF ERYTHROCYTE-DERIVED MICROPARTICLES FROM SICKLE CELL DISEASE PATIENTS IN THE STEADY STATE ON THROMBIN GENERATION AND EFFECTS OF HYDROXYUREA TREATMENT Patrick Van Dreden1, Aurelie Rousseau1, Ismail Elalamy2, Grigorios Gerotziafas2. 1Clinical Research Stago, Gennevilliers, France. 2APHP Hopital Tenon, Paris, France |
PROFILE OF THROMBIN GENERATION ASSAY AND THROMBOELASTOMETRY TO IDENTIFY WOMEN WITH MODERATE AND SEVERE PREECLAMPSIA. THE ROADMAP-PREECLAMPSIA STUDY Patrick Van Dreden1, 2, Elmina Lefkou3, Aurelie Rousseau1, Grigorios Gerotziafas2, 4. 1Clinical Research Diagnostica Stago, Gennevilliers, France. 2INSERM U938, Paris, France. 3Haematology Unit, Hippokration Hospital of Thessaloniki, Thessaloniki, Greece. 4Haematology-biology department Tenon hospital, Paris, France |
BURDEN OF DISEASE IN POTENTIAL PROPHYLAXIS-ELIGIBLE PATIENTS WITH VON WILLEBRAND DISEASE: POST-HOC ANALYSIS OF THE “COST OF VON WILLEBRAND DISEASE ACROSS EUROPE, A SOCIOECONOMIC STUDY” (CVESS) Ping Du1, George Morgan2, Sarah Brighton2, Francoise Truong Berthoz3, Nataliya Kemenyash3, Shawn X. Sun1. 1Takeda Development Center Americas, Inc, Cambridge, MA, USA. 2HCD Economics, Daresbury, United Kingdom. 3Takeda Pharmaceuticals International AG, Zurich, Switzerland |
BIOLOGICAL DIAGNOSIS OF THROMBOPHILIA IN CHILDREN: EXPERIENCE OF THE HEMATOLOGY LABORATORY OF THE IBN ROCHD UNIVERSITY HOSPITAL IN CASABLANCA Samy Ennachachibi1, 2, Hanaa Bencharef 1, 2, Bouchra Oukkache 1, 2. 1Hematology laboratory of CHU Ibn Rochd, Casablanca, Morocco. 2Hassan II University, Faculty of Medicine and Pharmacy of Casablanca, Casablanca, Morocco |
OXIDATIVE STRESS BIOMARKERS AND THEIR RELEVANCE TO FATTY ACID-BINDING PROTEIN IN STAGE-V CHRONIC KIDNEY DISEASE PATIENTS ON HEMODIALYSIS Divya Sridharan, Pranathi Karumanchi, Guy Olson. Loyola University of Chicago Stritch School of Medicine, Maywood, IL, USA |
F5_6755A>G, A NONSYNONYMOUS SINGLE-NUCLEOTIDE VARIATIONTHATSUBSTITUTES GLYCINE FOR ASPARTATE AT RESIDUE 2, 194 IN THE PLASMA BLOOD CLOTTING PROTEIN FACTOR V, IS PLEIOTROPICALLY ASSOCIATED WITH REDUCED FACTOR V COAGULANT ACTIVITY AND A DECREASED FRAILTY INDEX Hoang A. Nguyen1, Vincent P. Diego2, 3, Marcio A. Almeida2, 3, Shuchita Jhaveri1, Juan M. Peralta2, 3, Joanne E. Curran2, 3, Donna Lehman4, Ralph DeFronzo4, Miguel A. Escobar5, Raja Rajalingam6, Jerry S. Powell7, 8, Sarah Williams-Blangero2, 3, Ravindranath Duggirala2, 3, John Blangero2, 3, Tom Howard2, 3, 7, 9. 1University of Texas Rio Grande Valley (UTRGV) School of Medicine (SOM), Edinburg, TX, USA. 2Department of Human Genetics, UTRGV SOM, Brownsville, TX, USA. 3South Texas Diabetes and Obesity Institute, UTRGV SOM, Brownsville, TX, USA. 4University of Texas Health Science Center at San Antonio SOM, San Antonio, TX, USA. 5Division of Hematology and Oncology, Department of Internal Medicine, McGovern SOM, University of Texas Health Science Center at Houston, Houston, TX, USA. 6Immunogenetics and Transplantation Laboratory, Department of Surgery, School of Medicine, University of California at San Francisco, San Francisco, CA, USA. 7Haplogenics Corporation, Brownsville, TX, USA. 8Division of Hematology and Oncology, Department of Medicine, SOM, University of California at Davis, Davis, CA, USA. 9Department of Pathology and Laboratory Medicine, VA Texas Valley Coastal Bend Health Care System, Harlingen, TX, USA |
NEUTROPHIL PHENOTYPES CORRELATE WITH NET RELEASE AND PHOSPHATIDYLSERINE EXPOSURE Margaret H McKelvy, Madison G Chait, Madelaine E Duarte, Sanjay Khandelwal, Gowthami M Arepally, Grace M Lee. Division of Hematology, Duke University, Durham, NC, USA |
CORRELATION OF NF-KB AND D-DIMER WITH THE INCIDENCE OF DEEP VEIN THROMBOSIS IN HIGH-RISK THROMBOSIS CANCER PATIENTS Tri W Sukarnowati1, Budi Setiawan2, Daniel Rizqy1, Eko A Pangarsa2, Damai Santosa2, Catharina Suharti2. 1Trainee in Hematology-Medical Oncology, Internal Medicine Department, Faculty of Medicine Diponegoro University/Dr. Kariadi Hospital, Semarang, Indonesia. 2Hematology-Medical Oncology Division, Internal Medicine Department, Faculty of Medicine, Diponegoro University/Dr. Kariadi Hospital, Semarang, Indonesia |
COMPARISON OF HEPARIN DOSAGE IN CRITICALLY ILL CHILDREN Andrew Eckberg , Asavari Kamerkar, Eugene Laksana , Melissa Aczon, Randall Wetzel, David Ledbetter. Children's Hospital Los Angeles, Los Angeles, CA, USA |
BLEEDING OUTCOMES AND MANAGEMENT OF SUPRATHERAPEUTIC EPISODES SECONDARY TO WARFARIN IN PEDIATRICS: A SINGLE CENTER 11-YEAR EXPERIENCE Clay T Cohen1, HyoJeong Han1, Mark Zobeck1, Joseph A Spinner2, Jacquelyn M Powers1, YoungNa Lee-Kim1, Sarah E Sartain1. 1Department of Pediatrics, Division of Hematology/Oncology, Baylor College of Medicine, Texas Children's Hospital, Houston, TX, USA. 2Department of Pediatrics, Division of Cardiology, Baylor College of Medicine, Texas Children's Hospital, Houston, TX, USA |
BIO-EQUIVALENCE OF POTENCY ADJUSTEDAPPROVED HEPARIN SOLUTIONS COMPARED TOA NEWLY DEVELOPED HEPARIN SOLUTION. Debra Hoppensteadt1, Walter Jeske1, Ambar Farooqui1, Ahmed Kouta1, Omer Iqbal1, Bulent Kantarcioglu1, Roland Kraemer2, Jawed Fareed1, Guy Olson1. 1Loyola Univerity Chicago, Maywood, IL, USA. 2University of Heidelberg, Heidelberg Germany |
TECHNICAL FEASIBILITY AND CLINICAL EFFICACY OF ILIAC VEIN STENT PLACEMENT IN ADOLESCENTS WITH MAY-THURNER SYNDROME Frederic J. Bertino1, 2, C. Matthew Hawkins1, 2, Gary Woods1, 3, Jay H. Shah1, 2, Darshan E. Variyam1, 2, Anne E. Gill1, 2. 1CHILDREN'S HEALTHCARE OF ATLANTA, ATLANTA, GA, USA. 2Emory University SOM Dept. of Radiology and Imaging Sciences, Division of Interventional Radiology and Image Guided Medicine, Atlanta, GA, USA. 3Emory University School of Medicine, Department of Pediatrics, Division of Hematology and Oncology, Atlanta, GA, USA |
RETROSPECTIVE ANALYSIS OF HEREDITARY THROMBOPHILIA WORKUPS IN THE PEDIATRIC POPULATION OVER THREE YEARS: A SINGLE CENTER STUDY Hannah L McRae, Alexa Turgeman, Majed A Refaai. Department of Pathology and Laboratory Medicine, Transfusion Medicine Division, Hemostasis and Thrombosis Unit, University of Rochester Medical Center, Rochester, NY, USA |
INDIAN RECOMMENDATIONS ON ANTITHROMBOTIC MANAGEMENT FOR CHRONIC CORONARY SYNDROME: AN EXPERT CONSENSUS DELPHI STUDY Kamal Sharma1, Jay Shah2, Prakash Hazra3, Jagdish Hiremath4, Varun Narain5, Ashwani Mehta6, Ajit Bhagwat7, Aziz Khan8, Govindan Unni9, Tiny Nair10, Ajay Mahajan11, Ajay Naik12, K Kannan13, Monotosh Panja14, Prasant Kumar Sahoo Sahoo15, Subash Manchanda6. 1Dr. Kamal Sharma Cardiology Clinic, Ahmedabad, India. 2HCG Hospitals, Krish Heart Care, Ahmedabad, India. 3AMRI Hospitals, Kolkata, India. 4Ruby Hall, Pune, India. 5Divine Heart and Multispeciality Hospital, Lucknow, India. 6Sir Gangaram Hospital, Delhi, India. 7Kamalnayan Bajaj Hospital, Aurangabad, India. 8Crescent Hospital and Heart Centre, Nagpur, India. 9Jubilee Mission Hospital, Thrissur, India. 10PRS Hospital, Trivandrum, India. 11Cardiocare Heart Clinic, Mumbai, India. 12CIMS Hospital, AHMEDABAD, India. 13Stanley Medical College, Chennai, India. 14Belle Vue Clinic and AMRI Hospital, Kolkata, India. 15Apollo Hospital, Bhubneshwar, India |
VENOUS THROMBOEMBOLISM IN ADULT HOSPITALIZATIONS - UNITED STATES 2012-2019 Alys Adamski, Karon Abe, Nimia Reyes, Laura Schieve . Centers for Disease Control and Prevention, Atlanta, GA, USA |
VAGINAL BLOOD LOSS: A PATIENT- AND MEDICAL TRAINEE-CENTERED MIXED-METHODS RESEARCH PROGRAM Fartoon M Siad1, Romy Segall2, Andrea Lausman1, 3, Filomena Meffe1, 3, Carolyn Snider1, 4, Martina Trinkaus1, 5, Michelle Sholzberg1, 5. 1Department of Medicine, University of Toronto, Toronto, ON, Canada. 2Department of Medicine, Dalhousie University, Halifax, NS, Canada. 3Department of Obstetrics and Gynecology, University of Toronto, Toronto, ON, Canada. 4Division of Emergency Medicine, University of Toronto, Toronto, ON, Canada. 5Division of Hematology and Oncology, St. Michael, Toronto, ON, Canada |
VALIDATION OF PRODUCTION PROCESS OF THE FACTOR VIII COAGULATION Nataliia Shurko, Taras Danysh , Svitlana Myliashkevich, Vasyl Novak. State institution, Lviv, Ukrenia |
LOW INTENSITY HEPARIN INFUSION WAS ASSOCIATED WITH DECREASED MINOR BLEEDING AMONG PATIENTS WITH RECENT BLEEDING OR SURGERY, WITHOUT INCREASING THROMBOSIS. Niaima/Y Geresu3, Melissa/P Patel1, Danielle/N Martin3, Lester/T Piri3, Michael/D Knauss1, Bradley/L Smith1, Tony/Z Zhuang2, Mikhail/Y Akbashev2, 1. 1Grady Health System, Atlanta, GA, USA. 2Emory University School of Medicine, Atlanta, GA, USA. 3Mercer College of Pharmacy, Atlanta, GA, USA |
PATIENT-CENTRED CARE FOR WARFARIN MANAGEMENT: A PILOT STUDY TO TRANSITION CARE TO HIGH RISK PATIENTS Tammy J Bungard, Micheal S McMurtry, Steven R Meyer, Bruce Ritchie, Ross T Tsuyuki. University of Alberta, Edmonton, AB, Canada |
OPTIMIZATION OF STROKE PROPHYLAXIS FOR ATRIAL FIBRILLATION WITHIN CALGARY CO-OP: IMPACT OF A QUALITY IMPROVEMENT INITIATIVE Tammy J Bungard1, Sonal Ejner2. 1University of Alberta, Edmonton, AB, Canada. 2Calgary Co-operative Association Limited, Calgary, AB, Canada |